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KMID : 0352419930120010092
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Keimyung Medical Journal
1993 Volume.12 No. 1 p.92 ~ p.101
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A Clinical, Anthropometric, and Cephalometric Studies of Saethre-Chotzen Syndrome
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Abstract
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Saethre-Chotzen syndrome is characterized by a broad and variable pattern of malformations, including craniosynostosis, a low-set frontal hairline, facial asymmetry, ptosis of the eyelids, deviated nasal septum, brachydactyly, partial cutaneous
syndactyly and various skeletal anomalies. This syndrome is relatively common among craniosynostosis syndromes, however the condition may go unrecognized because of a relatively mild involvement of this syndrome and an erroneous diagnosis by
physician.
These authors have treated a 13-Year-old female patients having a widow's peak, a frontal upsweep of the anterior hairline, frontal bossing, a partial defect of the left eyebrow, an orbital hypertelorism, a telecanthus, an epicanthal fold, an
anti-mongoloid slant of the palpebral fissures, a flat nose, a mild parrot-beak nasal deformity, a notching deformity of the left alar nasi and asymmetric midface hypoplasia in addition to the general characteristics of the syndrome. An
unilateral
frontoorbital advancement with frontal remodeling, U-osteotomy, Mustarde's 4 flap Z-plasty, epicanthoplasty, augmentation rhinoplasty with an autogenous calvarial bone graft, face lift tripartite frontalis muscle transfer, and sliding dorsal flap
surgery was done in 2 separate stages. The preoperative appearance and the postoperative results at 24 months are evaluated by a clinical, anthropometric, and cephalometric analyses.
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KEYWORD
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